Infantile spasms

• What is another name for infantile spasms?

  West syndrome
• When do infantile spasms typically present?


  4 - 8 months of life
• Which sex is infantile spasms more common in?

  Males
• What are some features of infantile spasm?


  Characteristic 'salaam' attacks

  Lasts 1-2 seconds

  Progressive mental handicap
• What are some characteristics of a salaam attack?


  Flexion of head, trunk and arms followed by extension of the arms
• What are some investigations for infantile spasms?

  EEG

  CT
• What could an EEG show in those with infantile spasm?

  Hypsarrythmia
• What could a CT should in those wiht infantile spasm?


  Diffuse or localised brain disease
• What is considered first-line therapy in infantile spasm?

  Vigabatrin
• What is the management for infantile spasm?

  Vigabatrin

  ACTH
• What is the prognosis for infantile spasm?


  Poor