Complication of delayed treatment of Hirschsprung disease
Nursing action when patient experiences abdominal pain and vomiting
Start IV resuscitation
Appropriate nursing action is to encourage parents to ask questions and express concerns
Priority nursing intervention to monitor complications of Hirschsprung disease
Monitoring vital signs and response to interventions regularly
Nursing action to assess hydration status
Evaluate skin turgor and mucus membrane moisture
Nursing intervention to address baby's discomfort and promote rest
Encourage the parents to hold and comfort the baby as needed
Down syndrome
Chromosomal abnormality is Trisomy 21
Individuals with Down syndrome
Epicanthal folds are commonly seen
Developmental milestone delayed in babies with Down syndrome is walking
Effect of third copy of chromosome 21 in Down syndrome
Disrupts normal gene expression
Accommodations for individuals with Down syndrome in school
Providing visual aids and simplified instructions
Common health conditions associated with Down syndrome
Hearing loss
Visual problems
Prenatal screening for Down syndrome
Testing the levels of specific markers in maternal blood
Ethical considerations when discussing options for treatment of Down syndrome include the impact of test results on parental decision making
Hyperbilirubinemia
High levels of bilirubin in blood
Complication of severe untreated hyperbilirubinemia is Kernicterus
Hyperbilirubinemia in babies is dangerous and requires intensive care in the NICU under phototherapy
Purpose of phototherapy
Breaks down the bilirubin in the skin
Physiologic jaundice is not dangerous as it appears within the first 2 days after birth due to the immaturity of the baby's liver, but pathologic jaundice refers to hyperbilirubinemia
Management of hyperbilirubinemia
Exchange transfusion
Signs and symptoms of hyperbilirubinemia
Jaundice
Dark urine
Abdominal pain
A balanced diet with plenty of fruits and vegetables is beneficial for patients with hyperbilirubinemia
ABO incompatibility
Cause of jaundice in the first few weeks of life
ABO incompatibility between the mother and baby's blood type can cause the baby's jaundice
ABO incompatibility differs from Rh incompatibility in that Rh incompatibility leads to maternal sensitization while ABO does not
Lab test to confirm ABO incompatibility
Direct Coombs test
Nursing intervention for ABO incompatibility
Initiate phototherapy
Nursing intervention for breastfeeding to help jaundice
Monitor bilirubin levels closely and adjust feeding schedules accordingly
Hydrocephalus
Accumulation of excess CSF in ventricles or subarachnoid space
Reason for CSF accumulation in hydrocephalus is not the presence of infectious agents
Transillumination
Method of pointing a bright light against the skull
Clinical manifestations of hydrocephalus
Bulging eyes
Incision site for hydrocephalus surgery is at the posterior fontanelle
Early detection of hydrocephalus
Measure head circumference within an hour of birth and again before discharge
A diuretic might be prescribed for hydrocephalus
Increased intracranial pressure
Most important nursing diagnosis for hydrocephalus
Rationale for not allowing CSF to flow too rapidly during treatment is to prevent brain damage