Malformations of the head and neck include cysts, sinuses, and fistulas
Cyst
Epithelium lined cavity that does not have a internal or external opening
Sinus
Epithelium lined cavity that opens either internally or externally
Fistula
Epithelium lined tract that has both an internal and external opening
Malformations of the head and neck
Cyst
Sinus
Fistula
Branchial Cleft Cyst
Manifested between 15 and 25 years of age, both sexes equally affected, fistula more common than cyst, one of the main causes of neck swelling in children, rare for malignant transformation
Branchial Cleft Cyst
Persistence or incomplete regression of cervical sinus, internal fistula (2nd branchial pouch), external fistula (2nd branchial cleft)
Thyroglossal Duct Cyst and Fistula
75% before 5 years of age, most are diagnosed before 12 mos of age, malignant transformation rare
Thyroglossal Duct Cyst and Fistula
Incomplete obliteration or resorption of the thyroglossal duct
Lymphangioma
90% manifested in the first 2 years of life, tends to grow by expansion and infiltration, typically located in the lateral side of the neck, rarely undergoes spontaneous regression
Lymphangioma
Developed from sequestered portions of the primordial lymphatics, do not establish connection with venous system, degenerate to form cystic cavities
Hemangioma (hamartomas)
10% during first year of life, premature infants are predominantly affected, females (superficial hamartomas), 80% regress spontaneously
Hemangioma (hamartomas)
Dysontogenic growth of normally formed tissue, natural course: proliferative phase, stable plateu (lesion ceases growth), involutional growth
Hemangioma
10% during first year of life
Premature infants are predominantly affected
Females (superficial hamartomas)
80% regress spontaneously
Paraganglioma (glomus tumor)
Mostly solitary
10-20% malignant
Teratomas
Consist of all 3 germ layers (ecto, meso,ento)
5% of all congenital teratomas
Manifest before 12mos of age
Potential for malignant transformation
Dermoid
Composed mainly of ectodermal elements
Composed of dermal appendages (hair follicles, sebaceous gland, sweat glands)
Acute cervical lymphadenitis
"Reactive lymphadenitis" - Most common cause in children (streptococcal infection of the palatine tonsils)