"Animal starch". Storage form of CHO in the body found in the liver and muscle. Muscle glycogen supplies energy directly to surrounding tissues during work and exercise. Liver glycogen is converted to glucose to be used in the body through the process called "glycogenolysis". Source: liver, oysters, muscle meat. A glycogen storage disease (GSD, also glycogenosis and dextrinosis) is a metabolic disorder caused by enzyme deficiencies affecting either glycogen synthesis, glycogen breakdown, or glycolysis (glucose breakdown), typically within muscles and/or liver cells. GSD has two classes of causes: Genetic and Acquired. Glycogen storage disease type I (GSD I) or von Gierke disease, is the most common of the glycogen storage disease. This genetic disease results from the deficiency of the enzyme, glucose-6-phosphatase, and has an incidence in the American population of approximately 1 in 50,000 to 100,000 births.